Sickle Cell Anemia

History:

  • You are FY2 in General practice
  • A 30 year old carribean Afro woman has booked an appointment with concern.
  • She wants to become pregnant, her brother has sickle cell anemia, he has painful swelling in limbs , feels pain , and frequent infection.
  • She doesn’t have any of the symptoms, she reads some articles in the internet about sickle cell
  • She wants to know if her child will have sickle cell anemia or not
  • She is normally fit and well, no medical condition or allergy , no sign of anemia, married and lives with husband , he doesn’t have any family disease or sickle cell anemia.

Task:

  • Talk to the woman and address her concerns

Concern:

  • Will my baby get this too?

Management:

  • Greet and confirm identity
  • Explore her concerns, and ask how her brother is doing , what symptoms he has , and treatment , does any of other family member have the similar symptoms, or they screened for the sickle cell anaemia.
  • Ask about her partner , any symptom in him or in the family
  • Now appreciate her for taking decision for getting pregnant
  • Explain her this disease is caused by the gene that affects red blood cell, if both the parents have the gene there’s chance of 1 child among-st 4 will born with sickle cell anaemia
  • Rest of them can become carrier
  • sickle cell anaemia often detected during pregnancy and soon after birth , via heel prick test
  • Refer her and her husband to genetic counselling clinic for genetic testing for sickle cell anaemia
  • Tell her more about sickle cell society to learn more
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